2025
ICD-10-CM
Diagnosis
Code

D56.0 Alpha thalassemia

  • Billable
  • 2016–2025

D56.0 is a billable/specific diagnosis code from the 2025 ICD-10-CM used to classify the following condition: Alpha thalassemia.

Inclusion term

  • Alpha thalassemia major

  • Hemoglobin H Constant Spring

  • Hemoglobin H disease

  • Hydrops fetalis due to alpha thalassemia

  • Severe alpha thalassemia

  • Triple gene defect alpha thalassemia

Use additional code

  • Code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)

Type 1 excludes

  • Alpha thalassemia trait or minor (D56.3)

  • Asymptomatic alpha thalassemia (D56.3)

  • Hydrops fetalis due to isoimmunization (P56.0)

  • Hydrops fetalis not due to immune hemolysis (P83.2)

Versions

  1. 2025

    No changes

  2. 2024

    No changes

  3. 2023

    No changes

  4. 2022

    No changes

  5. 2021

    No changes

  6. 2020

    No changes

  7. 2019

    No changes

  8. 2018

    No changes

  9. 2017

    No changes

  10. 2016

    New code