D56.0 is a billable/specific diagnosis code from the 2025 ICD-10-CM used to classify the following condition: Alpha thalassemia.
Inclusion term
Alpha thalassemia major
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia
Use additional code
Code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
Type 1 excludes
Versions
2025
No changes
2024
No changes
2023
No changes
2022
No changes
2021
No changes
2020
No changes
2019
No changes
2018
No changes
2017
No changes
2016
New code