2025
ICD-10-CM
Diagnosis
Code

I27.29 Other secondary pulmonary hypertension

  • Billable
  • 2018–2025

I27.29 is a billable/specific diagnosis code from the 2025 ICD-10-CM used to classify the following condition: Other secondary pulmonary hypertension.

Inclusion term

  • Group 5 pulmonary hypertension

  • Pulmonary hypertension with unclear multifactorial mechanisms

  • Pulmonary hypertension due to hematologic disorders

  • Pulmonary hypertension due to metabolic disorders

  • Pulmonary hypertension due to other systemic disorders

Code also

  • Other associated disorders, if known, such as:

    • Chronic myeloid leukemia (C92.10-C92.22)

    • Essential thrombocythemia (D47.3)

    • Gaucher disease (E75.22)

    • Hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)

    • Hyperthyroidism (E05.-)

    • Hypothyroidism (E00-E03)

    • Polycythemia vera (D45)

    • Sarcoidosis (D86.-)

Versions

  1. 2025

    No changes

  2. 2024

    No changes

  3. 2023

    No changes

  4. 2022

    No changes

  5. 2021

    Code changed

    • Code also

        • other associated disorders, if known, such as:
        • chronic myeloid leukemia (C92.10- C92.22)
        • essential thrombocythemia (D47.3)
        • Gaucher disease (E75.22)
        • hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
        • hyperthyroidism (E05.-)
        • hypothyroidism (E00-E03)
        • polycythemia vera (D45)
        • sarcoidosis (D86.-)
        • other associated disorders, if known, such as:
        • chronic myeloid leukemia (C92.10-C92.22)
        • essential thrombocythemia (D47.3)
        • Gaucher disease (E75.22)
        • hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
        • hyperthyroidism (E05.-)
        • hypothyroidism (E00-E03)
        • polycythemia vera (D45)
        • sarcoidosis (D86.-)
  6. 2020

    No changes

  7. 2019

    Code changed

    • Code also

        • other associated disorders, if known, such as:
        • chronic myeloid leukemia (C92.10- C92.22)
        • essential thrombocythemia (D47.3)
        • Gaucher disease (E75.22)
        • hypertensive chronic kidney disease with end stage renal disease (I12.0, I12.11, I13.2)
        • hyperthyroidism (E05.-)
        • hypothyroidism (E00-E03)
        • polycythemia vera (D45)
        • sarcoidosis (D86.-)
        • other associated disorders, if known, such as:
        • chronic myeloid leukemia (C92.10- C92.22)
        • essential thrombocythemia (D47.3)
        • Gaucher disease (E75.22)
        • hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
        • hyperthyroidism (E05.-)
        • hypothyroidism (E00-E03)
        • polycythemia vera (D45)
        • sarcoidosis (D86.-)
  8. 2018

    New code