2025
ICD-10-CM
Diagnosis
Code

I27.83 Eisenmenger's syndrome

  • Billable
  • 2018–2025

I27.83 is a billable/specific diagnosis code from the 2025 ICD-10-CM used to classify the following condition: Eisenmenger's syndrome.

Inclusion term

  • Eisenmenger's complex

  • (Irreversible) Eisenmenger's disease

  • Pulmonary hypertension with right to left shunt related to congenital heart disease

Code also

  • Underlying heart defect, if known, such as:

    • Atrial septal defect (Q21.1-)

    • Eisenmenger's defect (Q21.8)

    • Patent ductus arteriosus (Q25.0)

    • Ventricular septal defect (Q21.0)

Versions

  1. 2025

    No changes

  2. 2024

    No changes

  3. 2023

    Code changed

    • Code also

        • underlying heart defect, if known, such as:
        • atrial septal defect (Q21.1)
        • Eisenmenger's defect (Q21.8)
        • patent ductus arteriosus (Q25.0)
        • ventricular septal defect (Q21.0)
        • underlying heart defect, if known, such as:
        • atrial septal defect (Q21.1-)
        • Eisenmenger's defect (Q21.8)
        • patent ductus arteriosus (Q25.0)
        • ventricular septal defect (Q21.0)
  4. 2022

    No changes

  5. 2021

    No changes

  6. 2020

    No changes

  7. 2019

    No changes

  8. 2018

    New code