M04.1 is a billable/specific diagnosis code from the 2025 ICD-10-CM used to classify the following condition: Periodic fever syndromes.
Inclusion term
Familial Mediterranean fever
Hyperimmunoglobin D syndrome
Mevalonate kinase deficiency
Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
Versions
2025
No changes
2024
No changes
2023
No changes
2022
No changes
2021
No changes
2020
No changes
2019
No changes
2018
No changes
2017
New code