Q82.2 is a billable/specific and POA-exempt diagnosis code from the 2025 ICD-10-CM used to classify the following condition: Congenital cutaneous mastocytosis.
Inclusion term
Congenital diffuse cutaneous mastocytosis
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa
Type 1 excludes
Versions
2025
No changes
2024
No changes
2023
No changes
2022
No changes
2021
No changes
2020
No changes
2019
No changes
2018
Code changed
Type 1 excludes
malignant mastocytosis (C96.2)
- cutaneous mastocytosis NOS (D47.01)
- diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
- malignant mastocytosis (C96.2-)
- systemic mastocytosis (D47.02)
- urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
Description
Mastocytosis
- Congenital cutaneous mastocytosis
Inclusion term
Urticaria pigmentosa
- Congenital diffuse cutaneous mastocytosis
- Congenital maculopapular cutaneous mastocytosis
- Congenital urticaria pigmentosa
Short description
Mastocytosis
- Congenital cutaneous mastocytosis
2017
No changes
2016
New code