2025
ICD-10-CM
Diagnosis
Code

Q82.2 Congenital cutaneous mastocytosis

  • Billable
  • POA Exempt
  • 2016–2025

Q82.2 is a billable/specific and POA-exempt diagnosis code from the 2025 ICD-10-CM used to classify the following condition: Congenital cutaneous mastocytosis.

Inclusion term

  • Congenital diffuse cutaneous mastocytosis

  • Congenital maculopapular cutaneous mastocytosis

  • Congenital urticaria pigmentosa

Type 1 excludes

  • Cutaneous mastocytosis NOS (D47.01)

  • Diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)

  • Malignant mastocytosis (C96.2-)

  • Systemic mastocytosis (D47.02)

  • Urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

Versions

  1. 2025

    No changes

  2. 2024

    No changes

  3. 2023

    No changes

  4. 2022

    No changes

  5. 2021

    No changes

  6. 2020

    No changes

  7. 2019

    No changes

  8. 2018

    Code changed

    • Type 1 excludes

        • malignant mastocytosis (C96.2)
        • cutaneous mastocytosis NOS (D47.01)
        • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
        • malignant mastocytosis (C96.2-)
        • systemic mastocytosis (D47.02)
        • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    • Description

        • Mastocytosis
        • Congenital cutaneous mastocytosis
    • Inclusion term

        • Urticaria pigmentosa
        • Congenital diffuse cutaneous mastocytosis
        • Congenital maculopapular cutaneous mastocytosis
        • Congenital urticaria pigmentosa
    • Short description

        • Mastocytosis
        • Congenital cutaneous mastocytosis
  9. 2017

    No changes

  10. 2016

    New code