2026
ICD-10-CM
Diagnosis
Code

Q89.81 Kabuki syndrome

  • Billable
  • POA Exempt
  • 2026–2026

Q89.81 is a new billable/specific and POA-exempt diagnosis code introduced in the 2026 ICD-10-CM used to classify the following condition: Kabuki syndrome.

Inclusion term

  • Kabuki syndrome, type 1, due to KMT2D mutation

  • Kabuki syndrome, type 2, due to KDM6A mutation

  • Niikawa-Kuroki syndrome

Versions

  1. 2026

    New code