2025
ICD-10-CM
Diagnosis
Code

E88.42 MERRF syndrome

  • Billable
  • 2016–2025

E88.42 is a billable/specific diagnosis code from the 2025 ICD-10-CM used to classify the following condition: MERRF syndrome.

Inclusion term

  • Myoclonic epilepsy associated with ragged-red fibers

Code also

  • Progressive myoclonic epilepsy (G40.3-)

Versions

  1. 2025

    No changes

  2. 2024

    No changes

  3. 2023

    No changes

  4. 2022

    No changes

  5. 2021

    No changes

  6. 2020

    No changes

  7. 2019

    No changes

  8. 2018

    No changes

  9. 2017

    Code changed

    • Code also

        • myoclonic epilepsy (G40.3-)
        • progressive myoclonic epilepsy (G40.3-)
  10. 2016

    New code