Type 1 excludes
Type 2 excludes
Ehlers-Danlos syndromes (Q79.6-)
Codes
E70
Disorders of aromatic amino-acid metabolism
E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E72
Other disorders of amino-acid metabolism
E73
Lactose intolerance
E74
Other disorders of carbohydrate metabolism
E75
Disorders of sphingolipid metabolism and other lipid storage disorders
E76
Disorders of glycosaminoglycan metabolism
E77
Disorders of glycoprotein metabolism
E78
Disorders of lipoprotein metabolism and other lipidemias
E79
Disorders of purine and pyrimidine metabolism
E80
Disorders of porphyrin and bilirubin metabolism
E83
Disorders of mineral metabolism
E84
Cystic fibrosis
E85
Amyloidosis
E86
Volume depletion
E87
Other disorders of fluid, electrolyte and acid-base balance
E88
Other and unspecified metabolic disorders
Versions
2025
No changes
2024
Code changed
Type 1 excludes
androgen insensitivity syndrome (E34.5-)congenital adrenal hyperplasia (E25.0)hemolytic anemias attributable to enzyme disorders (D55.-)Marfan's syndrome (Q87.4)5-alpha-reductase deficiency (E29.1)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
2023
No changes
2022
Code changed
Type 1 excludes
androgen insensitivity syndrome (E34.5-)congenital adrenal hyperplasia (E25.0)Ehlers-Danlos syndromes (Q79.6-)hemolytic anemias attributable to enzyme disorders (D55.-)Marfan's syndrome (Q87.4)5-alpha-reductase deficiency (E29.1)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
Type 2 excludes
- Ehlers-Danlos syndromes (Q79.6-)
2021
Code changed
Type 1 excludes
androgen insensitivity syndrome (E34.5-)congenital adrenal hyperplasia (E25.0)Ehlers-Danlos syndrome (Q79.6-)hemolytic anemias attributable to enzyme disorders (D55.-)Marfan's syndrome (Q87.4)5-alpha-reductase deficiency (E29.1)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndromes (Q79.6-)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
2020
Code changed
Type 1 excludes
androgen insensitivity syndrome (E34.5-)congenital adrenal hyperplasia (E25.0)Ehlers-Danlos syndrome (Q79.6)hemolytic anemias attributable to enzyme disorders (D55.-)Marfan's syndrome (Q87.4)5-alpha-reductase deficiency (E29.1)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndrome (Q79.6-)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
2019
No changes
2018
No changes
2017
No changes
2016
New code